Bilateral Temporal Bone Langerhans Cell Histiocytosis in a Two-Year-Old Boy

Histiocytosis X, or Langerhans cell histiocytosis (LCH), is a rare disease that consists of three less distinct, overlapping states: eosinophilic granuloma (EG), Hand-Schüller-Christian (HSC) disease, and LettererSiwe (LS) disease. Of the three, EG is the least severe and most localized form, and has the best prognosis. Temporal bone presentation is clinically similar to acute otomastoiditis. We diagnosed and treated without success a two-year-old patient with bilateral temporal bone LCH. From the Department of ENT/Head and Neck Clinic, From University Clinical Center, Prishtina, Kosova (A. Mustafa; Q. Hysenaj) A. Heta; H. Hundozi Hysenaj and Department of Human Pathology, University Clinical Center, Prishtina, Kosova (L. Gashi-Luci)